Kugelberg-Welander disease

noun

Ku·​gel·​berg-Wel·​an·​der disease ˈkü-gəl-ˌbərg-ˈvel-ən-dər- How to pronounce Kugelberg-Welander disease (audio)
: muscular weakness and atrophy that is caused by degeneration of motor neurons in the ventral horn of the spinal cord, is usually inherited as an autosomal recessive trait, and that becomes symptomatic during childhood or adolescence typically progressing slowly during adulthood compare werdnig-hoffmann disease

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Cite this Entry

“Kugelberg-Welander disease.” Merriam-Webster.com Medical Dictionary, Merriam-Webster, https://www.merriam-webster.com/medical/Kugelberg-Welander%20disease. Accessed 27 Apr. 2024.

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